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名词信息
中 文 名:
早老症
英 文 名:
progeria
中文又称:
中文曾称:
名词来源:
所属专业:
内分泌科
所属类别:
疾病诊断名词
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Pubmed相关的文献
progeria
相关文献:
Hutchinson-Gilford Progeria Syndrome: Cellular Mechanisms and Therapeutic Perspectives.
Cisneros B, García-Aguirre I, De Ita M, Arrieta-Cruz I, Rosas-Vargas H.
Arch Med Res. 2023 Jul;54(5):102837. doi: 10.1016/j.arcmed.2023.06.002. Epub 2023 Jun 28.
PMID:37390702
Hutchinson-Gilford Progeria Syndrome: A Premature Aging Disease.
Ahmed MS, Ikram S, Bibi N, Mir A.
Mol Neurobiol. 2018 May;55(5):4417-4427. doi: 10.1007/s12035-017-0610-7. Epub 2017 Jun 28.
PMID:28660486
Hutchinson-Gilford progeria syndrome.
Ullrich NJ, Gordon LB.
Handb Clin Neurol. 2015;132:249-64. doi: 10.1016/B978-0-444-62702-5.00018-4.
PMID:26564085
Hutchinson-Gilford Progeria Syndrome: A premature aging disease caused by LMNA gene mutations.
Gonzalo S, Kreienkamp R, Askjaer P.
Ageing Res Rev. 2017 Jan;33:18-29. doi: 10.1016/j.arr.2016.06.007. Epub 2016 Jun 29.
PMID:27374873
Doxycycline decelerates aging in progeria mice.
Wang M, Zhang J, Qiu J, Ma X, Xu C, Wu Q, Xing S, Chen X, Liu B.
Aging Cell. 2024 Jul;23(7):e14188. doi: 10.1111/acel.14188. Epub 2024 Apr 30.
PMID:38686927
Progeria-a Rare Genetic Condition with Accelerated Ageing Process.
Talukder P, Saha A, Roy S, Ghosh G, Dutta Roy D, Barua S.
Appl Biochem Biotechnol. 2023 Apr;195(4):2587-2596. doi: 10.1007/s12010-021-03514-y. Epub 2022 Apr 21.
PMID:35445924
The Molecular and Cellular Basis of Hutchinson-Gilford Progeria Syndrome and Potential Treatments.
Batista NJ, Desai SG, Perez AM, Finkelstein A, Radigan R, Singh M, Landman A, Drittel B, Abramov D, Ahsan M, Cornwell S, Zhang D.
Genes (Basel). 2023 Feb 27;14(3):602. doi: 10.3390/genes14030602.
PMID:36980874
Progeria.
Badame AJ.
Arch Dermatol. 1989 Apr;125(4):540-4.
PMID:2649013
First progeria monkey model generated using base editor.
Reddy P, Shao Y, Hernandez-Benitez R, Nuñez Delicado E, Izpisua Belmonte JC.
Protein Cell. 2020 Dec;11(12):862-865. doi: 10.1007/s13238-020-00765-z.
PMID:32729023
Mitophagy defect mediates the aging-associated hallmarks in Hutchinson-Gilford progeria syndrome.
Sun Y, Xu L, Li Y, Jia S, Wang G, Cen X, Xu Y, Cao Z, Wang J, Shen N, Hu L, Zhang J, Mao J, Xia H, Liu Z, Fu X.
Aging Cell. 2024 Jun;23(6):e14143. doi: 10.1111/acel.14143. Epub 2024 Mar 14.
PMID:38482753
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