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名词信息
中 文 名:
肺囊性纤维化
英 文 名:
pulmonary cystic fibrosis
中文又称:
囊性肺纤维化
中文曾称:
名词来源:
所属专业:
呼吸内科
所属类别:
疾病诊断名词
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Pubmed相关的文献
pulmonary cystic fibrosis
相关文献:
Acute Pulmonary Exacerbations in Cystic Fibrosis.
Goss CH.
Semin Respir Crit Care Med. 2019 Dec;40(6):792-803. doi: 10.1055/s-0039-1697975. Epub 2019 Oct 28.
PMID:31659730
Cystic Fibrosis Modulator Therapies.
Jia S, Taylor-Cousar JL.
Annu Rev Med. 2023 Jan 27;74:413-426. doi: 10.1146/annurev-med-042921-021447. Epub 2022 Aug 16.
PMID:35973718
Clinical Phenotypes of Cystic Fibrosis Carriers.
Polgreen PM, Comellas AP.
Annu Rev Med. 2022 Jan 27;73:563-574. doi: 10.1146/annurev-med-042120-020148.
PMID:35084992
Pulmonary Complications of Cystic Fibrosis.
Garcia B, Flume PA.
Semin Respir Crit Care Med. 2019 Dec;40(6):804-809. doi: 10.1055/s-0039-1697639. Epub 2019 Oct 28.
PMID:31659729
Cystic fibrosis: current concepts.
López-Valdez JA, Aguilar-Alonso LA, Gándara-Quezada V, Ruiz-Rico GE, Ávila-Soledad JM, Reyes AA, Pedroza-Jiménez FD.
Bol Med Hosp Infant Mex. 2021;78(6):584-596. doi: 10.24875/BMHIM.20000372.
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Cystic Fibrosis-Related Nontuberculous Mycobacterial Pulmonary Disease.
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Clin Chest Med. 2023 Dec;44(4):847-860. doi: 10.1016/j.ccm.2023.06.008. Epub 2023 Aug 14.
PMID:37890921
[Guideline for the diagnosis and treatment of patients with cystic fibrosis. Update].
Comité Nacional de Neumonología; Comité Nacional de Nutrición; Comité Nacional de Gastroenterología; Grupo de Trabajo de Kinesiología.
Arch Argent Pediatr. 2021 Feb;119(1):s17-s35. doi: 10.5546/aap.2021.s17.
PMID:33459002
Cystic fibrosis related diabetes: Medical management.
Ode KL, Chan CL, Granados A, Moheet A, Moran A, Brennan AL.
J Cyst Fibros. 2019 Oct;18 Suppl 2:S10-S18. doi: 10.1016/j.jcf.2019.08.003.
PMID:31679720
Outpatient management of pulmonary exacerbations in children with cystic fibrosis.
Perrem L, Martin I, Ratjen F.
Expert Rev Respir Med. 2023 Apr;17(4):295-304. doi: 10.1080/17476348.2023.2202852. Epub 2023 Apr 14.
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Diagnosing Cystic Fibrosis in Adults.
Barry PJ, Simmonds NJ.
Semin Respir Crit Care Med. 2023 Apr;44(2):242-251. doi: 10.1055/s-0042-1759881. Epub 2023 Jan 9.
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