Sotatercept for the Treatment of Pulmonary Arterial Hypertension.
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Pulmonary Arterial Hypertension and Hereditary Haemorrhagic Telangiectasia.
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Int J Mol Sci. 2018 Oct 17;19(10):3203. doi: 10.3390/ijms19103203.
Hereditary pulmonary arterial hypertension burden in pediatrics: A single referral center experience.
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Front Pediatr. 2023 Mar 29;11:1050706. doi: 10.3389/fped.2023.1050706. eCollection 2023.
Defining the clinical validity of genes reported to cause pulmonary arterial hypertension.
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Genet Med. 2023 Nov;25(11):100925. doi: 10.1016/j.gim.2023.100925. Epub 2023 Jul 5.
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Matsubara H, Ogawa A.
J Cardiol. 2014 Oct;64(4):243-9. doi: 10.1016/j.jjcc.2014.06.009. Epub 2014 Jul 28.
Single-Cell Imaging Maps Inflammatory Cell Subsets to Pulmonary Arterial Hypertension Vasculopathy.
Ferrian S, Cao A, McCaffrey EF, Saito T, Greenwald NF, Nicolls MR, Bruce T, Zamanian RT, Del Rosario P, Rabinovitch M, Angelo M.
Am J Respir Crit Care Med. 2024 Jan 15;209(2):206-218. doi: 10.1164/rccm.202209-1761OC.
Case report: Pulmonary arterial hypertension in ENG-related hereditary hemorrhagic telangiectasia.
Liu D, Xu F, Gao Q, Zhai Z.
Front Cardiovasc Med. 2022 Nov 10;9:1020762. doi: 10.3389/fcvm.2022.1020762. eCollection 2022.
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Avecilla V.
Int J Vasc Med. 2019 Jul 11;2019:2123906. doi: 10.1155/2019/2123906. eCollection 2019.
Pulmonary Idiopathic Hypertension.
Krowl L, Anjum F, Kaul P.
2023 Apr 27. In: StatPearls [Internet]. Treasure Island (FL): StatPearls Publishing; 2025 Jan–.
Pulmonary arterial hypertension in hereditary hemorrhagic telangiectasia associated with ACVRL1 mutation: a case report.
Walsh LJ, Collins C, Ibrahim H, Kerins DM, Brady AP, O Connor TM.
J Med Case Rep. 2022 Mar 1;16(1):99. doi: 10.1186/s13256-022-03296-9.
